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Desquamative interstitial pneumonitis and alveolar lipoproteinosis: Diagnostic difficulties and therapy problems with an infant

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Abstract

A desquamative, interstitial pneumonitis was diagnosed histologically in a 9-month-old boy who first became ill at the age of 5 weeks. The desquamative interstitial pneumonitis was associated with an acquired cytomegalovirus (CMV) infection. Despite treatment with corticoids, acyclovir and artificial ventilation, the patient died of pulmonary insufficiency at the age of 15 months. The autopsy revealed an alveolar lipoproteinosis.

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Abbreviations

DIP:

desquamative interstitial pneumonitis

UIP:

usual interstitial pneumonitis

ALP:

alveolar lipoproteinosis

CFR:

Complement fixing reaction

CMV:

cytomegalovirus infection

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Authors and Affiliations

  1. Children's University Hospital Munich, Dr. von Haunersches Kinderspital, Federal Republic of Germany

    K. Schneider, I. Brünstler, H. Vogel, H. Fendel & K. Remberger

  2. Department of Pathology of the University of Munich, Federal Republic of Germany

    K. Schneider, I. Brünstler, H. Vogel, H. Fendel & K. Remberger

  3. Children's Hospital St. Elisabeth, Neuburg, Federal Republic of Germany

    K. Schneider, I. Brünstler, H. Vogel, H. Fendel & K. Remberger

Authors
  1. K. Schneider
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  2. I. Brünstler
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  3. H. Vogel
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  4. H. Fendel
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  5. K. Remberger
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Schneider, K., Brünstler, I., Vogel, H. et al. Desquamative interstitial pneumonitis and alveolar lipoproteinosis: Diagnostic difficulties and therapy problems with an infant. Eur J Pediatr 145, 575–578 (1986). https://doi.org/10.1007/BF02429072

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  • DOI: https://doi.org/10.1007/BF02429072

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