Abstract
Omphalocele, also known as exomphalos, is an abdominal wall defect in which the intestines, liver, and occasionally other organs remain outside of the abdomen in a sac. The incidence of omphalocele is variable but generally occurs in 2.5/10,000 births. Small omphaloceles on the other hand occur with a rate of 1 case in 5000 live births. Large omphaloceles occur with a rate of 1 case in 10, 000 live births. The mean size of omphalocele defect is 2.5–5 cm (4–12 cm). Omphalocele is classified into two types: minor and major. The omphalocele sac is ruptured in 10–20 % of cases. This may occur in utero or during delivery.
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Recommended Reading
Ledbetter DJ. Gastroschisis and omphalocele. Surg Clin North Am. 2006;86:249–60.
Stoll C, Alembik Y, Dott B, Roth MP. Omphalocele and gastroschisis and associated malformations. Am J Med Genet A. 2008;146A(10):1280–5.
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Al-Salem, A. (2014). Omphalocele. In: An Illustrated Guide to Pediatric Surgery. Springer, Cham. https://doi.org/10.1007/978-3-319-06665-3_37
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DOI: https://doi.org/10.1007/978-3-319-06665-3_37
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