Synonym(s)
Lipogranulomatosis subcutanea; adipone-crosis subcutanea; lipophagic panniculitis of childhood
Definition
Panniculitis of children, characterized by subcutaneous nodules without systemic signs or symptoms
Pathogenesis
May be a variant of Weber-Christian disease; mechanism of disease unknown
Clinical manifestation
Well-demarcated, somewhat painful, symmetrical subcutaneous nodules, most often on lower extremities and trunk; atrophy in lesions of lipophagic panniculitis variant
Differential diagnosis
Thrombophlebitis; vasculitis; sarcoidosis; alpha-1 antitrypsin deficiency panniculitis; polyarteritis nodosa; eosinophilic fasciitis; eosinophilic myalgia syndrome; erythema induratum; erythema nodosum; leukemia; lipodermatosclerosis; lymphoma; pancreatic panniculitis; poststeroid panniculitis; scleroderma panniculitis; cytophagic histiocytic panniculitis; Sweet's syndrome
Therapy
No therapy indicated
References
Requena L, Sanchez Yus E (2001) Panniculitis. Part II. Mostly lobular panniculitis. Journal of the American Academy of Dermatology 45(3):325–361
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© 2004 Springer-Verlag
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(2004). Rothman-Makai syndrome. In: Levine, N., Levine, C.C. (eds) Dermatology Therapy. A to Z Essentials. Springer, Berlin, Heidelberg. https://doi.org/10.1007/3-540-29668-9_2366
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DOI: https://doi.org/10.1007/3-540-29668-9_2366
Publisher Name: Springer, Berlin, Heidelberg
Print ISBN: 978-3-540-00864-4
Online ISBN: 978-3-540-29668-3
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