Summary
Two sisters with documented Adamantiadis-Behcet's disease of different severity, associated with HLA-B51, are described. Although the overall incidence of this complex disease is not different between sexes, only 4 female siblings, versus 14 male, that fullfill the 1990's International Study Group for Behcet's Disease criteria have been reported in the literature.
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Vaiopoulos, G., Sfikakis, P.P., Hatzinikolaou, P. et al. Adamantiadis-Behcet's disease in sisters. Clin Rheumatol 15, 382–384 (1996). https://doi.org/10.1007/BF02230362
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DOI: https://doi.org/10.1007/BF02230362