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Pubertät – Normalität, Normvarianten und Abweichungen

Störungen der Pubertätsentwicklung sicher erkennen

Puberty—norms, normal variants, and disorders

Identifying pathologies of pubertal development

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Der Gynäkologe Aims and scope

Zusammenfassung

Weicht ein Mädchen in seiner Pubertätsentwicklung von der Peergroup ab, so kann dies zu erheblichem Leidensdruck führen. Nicht jede wahrgenommene Abweichung ist jedoch objektivierbar und nicht jede objektivierbare pathologisch. Neben Normvarianten können einer Pubertätstempostörung verschiedene, ganz unterschiedliche Erkrankungen zugrunde liegen. Die Ursachen reichen von „idiopathischen“ Störungen über endokrinologische, immunologische und genetische Erkrankungen, Tumoren bis hin zu psychosomatischen und psychiatrischen Krankheitsbildern. Im Beitrag wird die Abgrenzung einer möglichen Pathologie gegen die – sehr viel häufigeren – Normvarianten erläutert und die Differenzialdiagnosen der wichtigsten abklärungsbedürftigen, therapiepflichtigen Krankheitsbilder dargestellt.

Abstract

Deviation from the peer group in a girl’s pubertal development creates stress in the adolescent. However, not every subjectively perceived deviation is objectively manifest and not every proven deviation is associated with pathology. Besides variations of the norm, a large number of very different disorders can result in alteration of the onset and/or temporal course of pubertal development. These range from “idiopathic” disturbances, endocrinological and immunological diseases, genetic variations, and tumors, to psychosomatic and psychiatric diseases. In this article the emphasis is on distinguishing the more common and non-pathological variations of the norm from the various diseases that require further investigation and consequently treatment.

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  1. Praxis für Kinder- und Jugendmedizin, Kinderendokrinologie und Neonatologie, Lindenstr. 13, 23558, Lübeck, Deutschland

    Esther M. Nitsche

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Correspondence to Esther M. Nitsche.

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E.M. Nitsche gibt an, dass kein Interessenkonflikt besteht.

Für diesen Beitrag wurden vom Autor keine Studien an Menschen oder Tieren durchgeführt. Für die aufgeführten Studien gelten die jeweils dort angegebenen ethischen Richtlinien.

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Gisela Gille, Lüneburg

Katrin Schaudig, Hamburg

Anneliese Schwenkhagen, Hamburg

Aktualisierte Version der Originalpublikation von Nitsche EM (2017) Pubertätsstörungen beim Mädchen. Gynäkologe 50:867–878. https://doi.org/10.1007/s00129-017-4137-9

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Nitsche, E.M. Pubertät – Normalität, Normvarianten und Abweichungen. Gynäkologe 54, 626–639 (2021). https://doi.org/10.1007/s00129-021-04852-y

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