Abstract
Background
We present a giant clival chordoma with disseminated disease but without involvement of the clivus. To our knowledge, this is the youngest child and only the second case, presenting without base of skull involvement, in paediatric literature and the fourth reported case of a chordoma in a patient with tuberous sclerosis.
Discussion
We discuss the subtle presentation, difficulties in diagnosis and management and also review the literature.
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Acknowledgement
The authors wish to thank Dr. Rachael Brown for her kind assistance in providing photographs of representative histological slides.
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Kombogiorgas, D., St. George, E.J., Chapman, S. et al. Infantile clivus chordoma without clivus involvement: case report and review of the literature. Childs Nerv Syst 22, 1369–1374 (2006). https://doi.org/10.1007/s00381-006-0069-8
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DOI: https://doi.org/10.1007/s00381-006-0069-8