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Juvenile linear scleroderma with unique forms of renal involvement

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Abstract

Linear scleroderma is the most common type of juvenile localized scleroderma, which usually involves the limbs. The linear lesions may extend through the dermis, subcutaneous tissue, muscles, and the underlying bone, leading to significant functional and cosmetic deformities. Renal involvement in juvenile localized scleroderma is a rare manifestation. Here we report two cases with juvenile linear scleroderma and unique renal manifestations, including unilateral renal arterial stenosis and immunoglobulin M nephropathy.

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Authors and Affiliations

  1. Department of Pediatrics, School of Medicine, Dokuz Eylül University, Mithatpaşa Cad. 665/4, Küçükyalı, 35280, Izmir, Turkey

    Belde Kasap, Alper Soylu, Mehmet Türkmen & Salih Kavukcu

  2. Department of Radiology, School of Medicine, Dokuz Eylül University, Izmir, Turkey

    Yiğit Göktay

  3. Department of Pathology, School of Medicine, Dokuz Eylül University, Izmir, Turkey

    Sülen Sarıoğlu

  4. Department of Pediatrics, Izmir Tepecik Teaching and Research Hospital, Izmir, Turkey

    Can Öztürk

  5. Department of Pediatrics, Cerrahpaşa Medical Faculty, Istanbul University, Istanbul, Turkey

    Özgür Kasapçopur

Authors
  1. Belde Kasap
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  2. Alper Soylu
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  3. Mehmet Türkmen
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  4. Yiğit Göktay
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  5. Sülen Sarıoğlu
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  6. Can Öztürk
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  7. Özgür Kasapçopur
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  8. Salih Kavukcu
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Corresponding author

Correspondence to Salih Kavukcu.

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Kasap, B., Soylu, A., Türkmen, M. et al. Juvenile linear scleroderma with unique forms of renal involvement. Pediatr Nephrol 24, 2041–2045 (2009). https://doi.org/10.1007/s00467-009-1206-x

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  • DOI: https://doi.org/10.1007/s00467-009-1206-x

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