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Neurocognition in Mitochondrial Disorders

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Handbook of Medical Neuropsychology

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Abstract

A mitochondrion (plural mitochondria) is a specialized cellular subunit found in most living cells. Mitochondria generate most of a cell’s supply of adenosine triphosphate (ATP) and supply the cell with energy primarily derived from oxidation of carbohydrates and fatty acids in the mitochondria. A mitochondrion has its own DNA and its own transcription and translation processes. The mitochondrial DNA encodes only 13 polypeptides which are located in the inner mitochondrial membrane as subunits of the respiratory chain complexes.

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Authors and Affiliations

  1. Department of Psychiatry and Behavioral Sciences, State University of New York – Upstate Medical University, Syracuse, NY, 13210, USA

    Kevin M. Antshel

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  1. Kevin M. Antshel
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Correspondence to Kevin M. Antshel .

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Editors and Affiliations

  1. Division of Oncology, Children's Hospital of Philadelphia, Market Street 3535, Philadelphia, 19104, USA

    Carol L. Armstrong

  2. Western Psychiatric Institute and Clinic, 3811 O'Hara Street, Pittsburgh, 15213, USA

    Lisa Morrow

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Antshel, K.M. (2010). Neurocognition in Mitochondrial Disorders. In: Armstrong, C., Morrow, L. (eds) Handbook of Medical Neuropsychology. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-1364-7_27

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