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Cystic Hygroma and Lymphatic Malformations

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Rickham's Neonatal Surgery

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Abstract

Lymphatic malformations (LMs) are uncommon congenital low-flow vascular anomalies previously referred to as lymphangiomas or cystic hygromas. The terminology of vascular and lymphatic lesions needs to be standardized. Vascular and lymphatic lesions, in general, have been notoriously difficult for pathologists to diagnose and classify because of the large number of entities and their variants, and their frequently overlapping clinical and histopathologic features. This problem has been compounded by imprecise terminology with various names referring to the same lesion or, conversely, a particular term denoting different entities. Recently, the International Society for the Study of Vascular Anomalies (ISSVA), an organization comprised of specialists in various disciplines interested in vascular anomalies, approved a novel classification of vascular lesions that distinguishes malformations from tumors and provides an easily understood and concise nomenclature.

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Author information

Authors and Affiliations

  1. Pediatric Surgery, Jichi Medical University, Tochigi, Japan

    Shigeru Ono MD, PhD

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  1. Shigeru Ono MD, PhD
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Correspondence to Shigeru Ono MD, PhD .

Editor information

Editors and Affiliations

  1. Division of Child Health, Alder Hey Children’s NHS Foundation Trust, Liverpool, United Kingdom

    Paul D. Losty

  2. University of Pennsylvania , Philadelphia, Pennsylvania, USA

    Alan W. Flake

  3. Childrens Hospital, University of Helsinki, Helsinki, Finland

    Risto J. Rintala

  4. Royal Children’s Hospital, University of Melbourne, Parkville, Victoria, Australia

    John M. Hutson

  5. Department of Surgery, Meiji University of Integrative Medicine, Kyoto, Japan

    Naomi lwai

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Ono, S. (2018). Cystic Hygroma and Lymphatic Malformations. In: Losty, P., Flake, A., Rintala, R., Hutson, J., lwai, N. (eds) Rickham's Neonatal Surgery. Springer, London. https://doi.org/10.1007/978-1-4471-4721-3_55

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  • DOI: https://doi.org/10.1007/978-1-4471-4721-3_55

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