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Idiopathic Pulmonary Fibrosis Phenotypes

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Idiopathic Pulmonary Fibrosis

Part of the book series: Respiratory Medicine ((RM,volume 9))

Abstract

Idiopathic pulmonary fibrosis is a distinct progressive fibrotic disorder that is characterized by heterogeneity in its presentation, clinical course, pathology, and other nuanced features. This has resulted in the recognition of distinct clinical phenotypes within the rubric of this disorder. Phenotypes may be recognized based on clinical features, physiologic testing, radiographic appearance, or patients’ subsequent disease course. This chapter will discuss the various IPF phenotypes and their unique distinguishing features.

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Authors and Affiliations

  1. Advanced Lung Disease and Lung Transplant Program, Department of Medicine, Inova Fairfax Hospital, 3300 Gallows Road, Falls Church, VA, 22042, USA

    Steven D. Nathan M.D.

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Correspondence to Steven D. Nathan M.D. .

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Editors and Affiliations

  1. Dept. Internal Medicine, Sect. Allergy Pulmonary & Critical Care Med., University of Wisconsin School of Medicine & Public Health, Madison, Wisconsin, USA

    Keith C. Meyer

  2. Advanced Lung Disease and Lung Transplant Program, Inova Fairfax Hospital, Falls Church, Virginia, USA

    Steven D. Nathan

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Nathan, S.D. (2014). Idiopathic Pulmonary Fibrosis Phenotypes. In: Meyer, K., Nathan, S. (eds) Idiopathic Pulmonary Fibrosis. Respiratory Medicine, vol 9. Humana Press, Totowa, NJ. https://doi.org/10.1007/978-1-62703-682-5_10

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  • DOI: https://doi.org/10.1007/978-1-62703-682-5_10

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