Abstract
Omenn syndrome is a rare and severe combined immunodeficiency disease, with an early onset, desquamative erythroderma, hepatosplenic lymphadenopathy, eosinophilia, diarrhea, IgE Increased, loss of B lymphocytes, severe damage to T and B lymphocytes. The prognosis of this disease is poor, and death is often caused by organ failure and severe infection. Here we reported a case of omenn syndrome with generalized erythema, and review the literature of omenn syndrome briefly.
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Yue, SZ., Luo, YY., Tang, JP., Zhou, B. (2022). A Girl with Erythema all Over the Body. In: Satolli, F., Tirant, M., Wollina, U., Lotti, T.M. (eds) Clinical Cases in Pediatric Skin Cancers. Clinical Cases in Dermatology. Springer, Cham. https://doi.org/10.1007/978-3-030-93666-2_10
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DOI: https://doi.org/10.1007/978-3-030-93666-2_10
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