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Noninvasive Mechanical Ventilation in Patients with Neuromuscular Disease

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Noninvasive Mechanical Ventilation and Difficult Weaning in Critical Care

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Abstract

Respiratory failure is the most common cause of morbidity and mortality in patients with progressive neuromuscular diseases (NMDs) [1–4]. The wide variety of NMDs that can affect respiratory function are listed in Table 32.1. NMDs are often complicated by progressive involvement of the respiratory muscles and can lead to both chronic and acute respiratory failure (ARF). Reduced inspiratory muscle strength can result in ineffective alveolar ventilation, and weakness of expiratory muscles can lead to inadequate clearance of airway secretions. Thus, these conditions can cause chronic respiratory failure as well as potentially life-threatening problems [5–10].

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Authors and Affiliations

  1. Anesthesiology and Intensive Care Unit, SS Antonio Biagio e Cesare Arrigo Hospital, Alessandria, Italy

    Fabrizio Racca MD, Chiara Robba & Maria Pia Dusio

  2. S.C. Anestesia e Rianimazione Pediatrica Azienda Ospedaliera SS Antonio Biagio e Cesare Arrigo, Via Venezia 16, 15100, Alessandria, Italy

    Fabrizio Racca MD

Authors
  1. Fabrizio Racca MD
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  2. Chiara Robba
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  3. Maria Pia Dusio
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Correspondence to Fabrizio Racca MD .

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Editors and Affiliations

  1. Hospital Morales Meseguer Intensive Care Unit, Murcia, Spain

    Antonio M. Esquinas

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Racca, F., Robba, C., Dusio, M.P. (2016). Noninvasive Mechanical Ventilation in Patients with Neuromuscular Disease. In: Esquinas, A. (eds) Noninvasive Mechanical Ventilation and Difficult Weaning in Critical Care. Springer, Cham. https://doi.org/10.1007/978-3-319-04259-6_32

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  • DOI: https://doi.org/10.1007/978-3-319-04259-6_32

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-04258-9

  • Online ISBN: 978-3-319-04259-6

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