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Blau Syndrome

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Intraocular Inflammation

Abstract

Blau syndrome is an autosomal dominant disease which characteristically results in a granulomatous rash, arthritis, and uveitis. Blau syndrome was first described in 1985 in two separate reports. Although the description by Jabs and colleagues appeared first, the eponym, Blau, is widely applied to this syndrome. Many prefer the term, pediatric granulomatous arthritis and uveitis to the name, Blau [15].

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Correspondence to James T. Rosenbaum MD .

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Rosenbaum, J.T., Rosenzweig, H.L., Martin, T.M. (2016). Blau Syndrome. In: Zierhut, M., Pavesio, C., Ohno, S., Orefice, F., Rao, N. (eds) Intraocular Inflammation. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-75387-2_77

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  • DOI: https://doi.org/10.1007/978-3-540-75387-2_77

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-540-75385-8

  • Online ISBN: 978-3-540-75387-2

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