Abstract
Neuromuscular scoliosis proves itself to be a challenge due to many facts. Among these are the usually early age of onset, rapid progression, rigidity, and lack of response to brace treatment. Added to that the inherent problems present in an already sick child, surgical interventions become perilous. Meningomyelocele patients provide an additional challenge by their lack of posterior anchor points for instrumentation and difficulty in achieving soft-tissue coverage. Neurofibromatosis type-1 scoliosis often accompanies preexisting neurological deficits, neurofibromas, rib protrusion into the spinal canal, and others. Arthrogryposis syndromes with multiple joint contractures and micrognathia may make intubation and patient positioning a challenge before surgery is even begun. Growth-retaining constructs such as the VEPTR and double growing rods represent the current mainstay of surgical treatment, barring specific contraindications unique to the disorder at hand.
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Hasler, CC. (2011). Other Neuromuscular Disorders with Scoliosis. In: Yazici, M. (eds) Non-Idiopathic Spine Deformities in Young Children. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-19417-7_8
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DOI: https://doi.org/10.1007/978-3-642-19417-7_8
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