Abstract
Atypical Teratoid/Rhabdoid tumors (AT/RT) of the CNS are highly malignant (WHO grade IV) heterogeneous embryonal tumors (ICD-Code 9508/3 WHO classification 2007), which are diagnosed with an increasing frequency. Their incidence in large series is estimated to be 1–2% of pediatric brain tumors but the incidence is about tenfold in children below the age of 3 years, when the diagnosis is as common as medulloblastoma. Although the imaging features have always been described as non-specific there seem to be certain morphological markers that are more frequently observed in AT/RT than in other brain tumors of childhood. Along with the clinical data of a patient i.e. young age, metastatic lesion, aggressive neoplasm suggestive features on Magnetic Resonance Imaging (MRI) and Computed Tomography (CT) are presented and make the diagnosis possible in many cases.
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Warmuth-Metz, M., Frühwald, M. (2012). Pediatric Atypical Teratoid/Rhabdoid Tumors: Imaging with CT and MRI. In: Hayat, M. (eds) Pediatric Cancer, Volume 2. Pediatric Cancer, vol 2. Springer, Dordrecht. https://doi.org/10.1007/978-94-007-2957-5_4
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DOI: https://doi.org/10.1007/978-94-007-2957-5_4
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