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Cutaneous Vasculitis

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Atlas of Genetic Diagnosis and Counseling

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Abstract

Vasculitis, inflammation of the vessel wall, can result in mural destruction with hemorrhage, aneurysm formation, and infarction, or intimal-medial hyperplasia and subsequent stenosis leading to tissue ischemia and infarction. The skin, in part due to its large vascular bed, exposure to cold temperatures, and frequent presence of stasis, is involved in many distinct as well as unnamed vasculitic syndromes that vary from localized and self-limited to generalized and life-threatening with multi-organ disease. Cutaneous vasculitis comprises a wide spectrum of overlapping primary and secondary disease entities that are characterized by predominant skin involvement and varying degrees of systemic manifestations (Carlson et al. 2005).

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Authors and Affiliations

  1. Medical Genetics, Shriners Hospitals for Children, Shreveport, LA, USA

    Harold Chen

  2. Perinatal and Clinical Genetics, Department of Pediatrics, LSU Health Sciences Center, 1501 Kings Highway, 71130, Shreveport, LA, USA

    Harold Chen

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  1. Harold Chen
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Correspondence to Harold Chen .

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Chen, H. (2015). Cutaneous Vasculitis. In: Atlas of Genetic Diagnosis and Counseling. Springer, New York, NY. https://doi.org/10.1007/978-1-4614-6430-3_256-1

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  • DOI: https://doi.org/10.1007/978-1-4614-6430-3_256-1

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  • Publisher Name: Springer, New York, NY

  • Online ISBN: 978-1-4614-6430-3

  • eBook Packages: Springer Reference Biomedicine and Life SciencesReference Module Biomedical and Life Sciences

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