Abstract
The spectrum of congenital mitral valve stenosis (MS) consists of a complex of defects that result in obstruction to left ventricular inflow. This spectrum includes patients with underdeveloped left heart structures (Fig. 1) to those with isolated congenital MS. The specific mitral valve defects can further be divided into categories based on the relationship to the mitral valve annulus including valvar, supravalvar and subvalvar components. Clinically, these patients present based on the degree of obstruction, associated mitral regurgitation, secondary pulmonary hypertension, associated lung disease and/or associated cardiac lesions. There are a number of factors that contribute to the successful outcomes in these patients including pre-operative imaging, aggressive surgical techniques and peri-operative management.
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Christopher W. Baird, Gerald R. Marx, Michele Borisuk, Sitaram Emani and Pedro J. del Nido declare that they have no conflicts of interest.
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Associate Editor Ajit P. Yoganathan oversaw the review of this article.
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Baird, C.W., Marx, G.R., Borisuk, M. et al. Review of Congenital Mitral Valve Stenosis: Analysis, Repair Techniques and Outcomes. Cardiovasc Eng Tech 6, 167–173 (2015). https://doi.org/10.1007/s13239-015-0223-0
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DOI: https://doi.org/10.1007/s13239-015-0223-0