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Congenital Hepatic Vascular Malformations

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Vascular Liver Disease

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Abstract

Congenital hepatic vascular malformations are rare entities that result in abnormal shunting of blood through the liver. Three different types of shunting can occur: arteriovenous (hepatic artery to hepatic vein), arterioportal (hepatic artery to portal vein) and portovenous (portal vein to hepatic vein). Malformations result from alterations in the formation of blood vessels during fetal development and can occur as an isolated abnormality or form a part of a systemic illness, such as hereditary hemorrhagic telangiectasia in which all three types of shunting coexist. Clinical features depend on the type and extent of shunting.

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Authors and Affiliations

  1. Section of Digestive Diseases, Yale University School of Medicine, 333 Cedar Street, LMP 1080, New Haven, CT, 06520, USA

    Guadalupe Garcia-Tsao

  2. Section of Digestive Diseases, VA Connecticut Health Care System, West Haven, CT, USA

    Guadalupe Garcia-Tsao

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  1. Keck School of Medicine, Div. GI & Liver Diseases, University of Southern California, Los Angeles, 90033, California, USA

    Laurie D. DeLeve

  2. , Section of Digestive Diseases, Yale University School of Medicine, New Haven, 06520, Connecticut, USA

    Guadalupe Garcia-Tsao

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Garcia-Tsao, G. (2011). Congenital Hepatic Vascular Malformations. In: DeLeve, L., Garcia-Tsao, G. (eds) Vascular Liver Disease. Springer, New York, NY. https://doi.org/10.1007/978-1-4419-8327-5_14

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  • Print ISBN: 978-1-4419-8326-8

  • Online ISBN: 978-1-4419-8327-5

  • eBook Packages: MedicineMedicine (R0)

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