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Uhl Anomaly

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CT Atlas of Adult Congenital Heart Disease

Abstract

Uhl anomaly is a very rare condition characterized by complete or partial absence of the right ventricular myocardium, which is replaced by fibroelastic tissue [1].

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References

  1. Uhl HSM. A previously undescribed congenital malformation of the heart: almost total absence of the myocardium of the right ventricle. Bull Johns Hopkins Hosp. 1952;91:197–205.

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Authors and Affiliations

  1. The Christ Hospital Heart and Vascular Center of Greater Cincinnati, The Lindner Center for Research and Education, Cincinnati, OH, USA

    Wojciech Mazur & Robert Pelberg

  2. Mallinckrodt Institute of Radiology, Washington University School of Medicine, St. Louis, Missouri, USA

    Marilyn J. Siegel

  3. Department of Clinical Radiology and Imaging Diagnostics, 4th Military Hospital, Wrocław, Poland

    Tomasz Miszalski-Jamka

  4. Center for Diagnosis Prevention and Telemedicine, John Paul II Hospital, Kraków, Poland

    Tomasz Miszalski-Jamka

Authors
  1. Wojciech Mazur
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  2. Marilyn J. Siegel
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  3. Tomasz Miszalski-Jamka
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  4. Robert Pelberg
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© 2013 Springer-Verlag London

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Mazur, W., Siegel, M.J., Miszalski-Jamka, T., Pelberg, R. (2013). Uhl Anomaly. In: CT Atlas of Adult Congenital Heart Disease. Springer, London. https://doi.org/10.1007/978-1-4471-5088-6_8

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  • DOI: https://doi.org/10.1007/978-1-4471-5088-6_8

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  • Publisher Name: Springer, London

  • Print ISBN: 978-1-4471-5087-9

  • Online ISBN: 978-1-4471-5088-6

  • eBook Packages: MedicineMedicine (R0)

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