Abstract
Multiple osteochondromatosis is a familial disease characterized by multiple osteochondromas, defect in metaphyseal remodeling, and asymmetric longitudinal growth retardation. There is a greater incidence in males than females (7:3). It was often first discovered at a younger age than solitary form. There is a predilection for the metaphyseal regions around the knee, hip, and shoulder joints. Radiologically individual lesions are similar to those of solitary form.
The lesions have the same gross and microscopic appearances as seen in solitary osteochondroma. The development of secondary malignancy varies from 5 % to 25 %. The treatment should be considered to correct deformities or functional disturbances.
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Park, YK. (2015). Multiple Osteochondromatosis. In: Santini-Araujo, E., Kalil, R., Bertoni, F., Park, YK. (eds) Tumors and Tumor-Like Lesions of Bone. Springer, London. https://doi.org/10.1007/978-1-4471-6578-1_20
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DOI: https://doi.org/10.1007/978-1-4471-6578-1_20
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