Abstract
Angiosarcoma is a high-grade malignant neoplasia characterized by cells with endothelial differentiation. It is rare in bone, usually seen in adult patients, affecting bones of the extremities, especially the femur, followed by the pelvis and axial skeleton. Most cases are unifocal but can be multifocal. It is usually painful. Its cells express endothelial markers, its epithelioid variant also expressing epithelial markers. Angiosarcoma is a very aggressive neoplasia, and its eventual multifocality makes it difficult or impossible to control; the prognosis is dismal in most cases.
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Kalil, R.K. (2015). Angiosarcoma. In: Santini-Araujo, E., Kalil, R., Bertoni, F., Park, YK. (eds) Tumors and Tumor-Like Lesions of Bone. Springer, London. https://doi.org/10.1007/978-1-4471-6578-1_36
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DOI: https://doi.org/10.1007/978-1-4471-6578-1_36
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