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Familial Dysautonomia and Other Congenital Sensory and Autonomic Neuropathies

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Cellular and Molecular Biology of Neuronal Development

Abstract

Since we are concerned at this conference with neuronal development, it is appropriate to consider those human disorders that may represent aberrations in development or function. These would be the congenital sensory neuropathies, rather than those that are acquired or of adult onset. Congenital sensory neuropathies are rare and can present as diagnostic problems, since analgesia and autonomic function are difficult to evaluate objectively in the young child. Controversy over terminology further confuses classification of the congenital sensory neuropathies (Axelrod, 1983; Dyck and Ohta, 1975).

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Author information

Authors and Affiliations

  1. Department of Pediatrics, New York University School of Medicine, New York, New York, 10016, USA

    Felicia B. Axelrod

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  1. Felicia B. Axelrod
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Editor information

Editors and Affiliations

  1. Cornell University Medical College, New York, New York, USA

    Ira B. Black

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© 1984 Plenum Press, New York

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Axelrod, F.B. (1984). Familial Dysautonomia and Other Congenital Sensory and Autonomic Neuropathies. In: Black, I.B. (eds) Cellular and Molecular Biology of Neuronal Development. Springer, Boston, MA. https://doi.org/10.1007/978-1-4613-2717-2_21

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  • DOI: https://doi.org/10.1007/978-1-4613-2717-2_21

  • Publisher Name: Springer, Boston, MA

  • Print ISBN: 978-1-4612-9686-7

  • Online ISBN: 978-1-4613-2717-2

  • eBook Packages: Springer Book Archive

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