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Chronic Thromboembolic Pulmonary Hypertension

  • Chapter
Management of Acute Pulmonary Embolism

Part of the book series: Contemporary Cardiology ((CONCARD))

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Abstract

Chronic thromboembolic pulmonary hypertension (CTEPH) is a poorly understood disorder. It is characterized by pulmonary hypertension associated with an apparent failure to resolve extensive, typically major-vessel pulmonary thromboemboli. Although CTEPH is believed to be a thromboembolic disease, the typical risk factors for venous thromboembolism are absent. According to the 2003 Venice classification of pulmonary hypertension, CTEPH represents group IV of pulmonary hypertensive diseases and thus does not rank as a subgroup of pulmonary arterial hypertension. Since 2003, however, it is well recognized that CTEPH predominantly results in changes in the major pulmonary artieries, in combination with significant pulmonary vascular disease, which is indistinguishable from classic idiopathic pulmonary hypertension. The present review provides an update on our current knowledge of the pathophysiology, diagnosis, and treatment options for CTEPH.

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Authors and Affiliations

  1. Department of Cardiology, Medical University of Vienna, Austria

    Irene M. Lang MD

  2. Department of Cardiothoracic Surgery, Medical University of Vienna, Austria

    Walter Klepetko MD

Authors
  1. Irene M. Lang MD
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  2. Walter Klepetko MD
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Editors and Affiliations

  1. Department of Cardiology and Pulmonology, Georg August University, Goettingen, Germany

    Stavros V. Konstantinides MD (Professor of Medicine) (Professor of Medicine)

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© 2007 Humana Press Inc., Totowa, NJ

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Lang, I.M., Klepetko, W. (2007). Chronic Thromboembolic Pulmonary Hypertension. In: Konstantinides, S.V. (eds) Management of Acute Pulmonary Embolism. Contemporary Cardiology. Humana Press. https://doi.org/10.1007/978-1-59745-287-8_19

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  • DOI: https://doi.org/10.1007/978-1-59745-287-8_19

  • Publisher Name: Humana Press

  • Print ISBN: 978-1-58829-644-3

  • Online ISBN: 978-1-59745-287-8

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