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Rare Malignancies of the Kidney: Evaluation and Management

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Clinical Management of Renal Tumors

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Abstract

Up to twenty percent of renal masses suspicious for renal cell carcinoma in adults are not RCC upon final pathology. While many of these tumors are benign, those that are malignant tend to be aggressive and lethal. Rare malignancies can often be diagnosed with renal biopsy. Many of these malignancies require additional or alternative oncologic therapies and close collaboration with medical and/or radiation oncologists. This chapter reviews the pathologic, diagnostic, therapeutic, including surgical and non-surgical approaches, and prognostic considerations pertaining to these uncommon renal malignancies. Covered are renal sarcoma, renal lymphoma, metastatic disease, carcinoid adult Wilms’ tumor, primitive neuroendocrine tumor, and small cell carcinoma.

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Authors and Affiliations

  1. Department of Urology, Loyola University Medical Center, Maywood, IL

    Kristian R. Novakovic MD

  2. Department of Urology, Cleveland Clinic Foundation, Cleveland, OH

    Steven C. Campbell MD, PhD

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  1. Kristian R. Novakovic MD
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  2. Steven C. Campbell MD, PhD
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Editors and Affiliations

  1. Taussig Cancer Center, Cleveland Clinic Foundation, Cleveland, OH

    Ronald M. Bukowski MD

  2. Glickman Urological and Kidney Institute, Cleveland Clinic Foundation, Cleveland, OH

    Andrew C. Novick MD

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Novakovic, K.R., Campbell, S.C. (2008). Rare Malignancies of the Kidney: Evaluation and Management . In: Bukowski, R.M., Novick, A.C. (eds) Clinical Management of Renal Tumors. Humana Press. https://doi.org/10.1007/978-1-60327-149-3_38

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  • DOI: https://doi.org/10.1007/978-1-60327-149-3_38

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