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Epidemiology of FMF Worldwide

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Familial Mediterranean Fever

Part of the book series: Rare Diseases of the Immune System ((RDIS,volume 3))

Abstract

The familial Mediterranean fever (FMF) is the primarily described and most prevalent autoinflammatory disease known in the world. FMF was so named by Heller, because of its high prevalence in the Mediterranean population [1]. Indeed, it was previously denominated as benign paroxysmal peritonitis by Siegal, a New York allergist of Jewish origin [2], whereas it has been described as Maladie periodique by French authors [3].

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Authors and Affiliations

  1. Department of Internal Medicine, Periodic Fever Research Centre, Catholic University of Sacred Heart, L.go F. Vito, 1, Rome, 00168, Italy

    Lucia Cerrito, Ludovico Luca Sicignano, Elena Verrecchia & Raffaele Manna

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  1. Lucia Cerrito
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  2. Ludovico Luca Sicignano
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  3. Elena Verrecchia
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  4. Raffaele Manna
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Correspondence to Raffaele Manna .

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Editors and Affiliations

  1. II Paediatric Unit-Rheumatology, G. Gaslini Institute, Genova, Genova, Italy

    Marco Gattorno

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Cerrito, L., Sicignano, L.L., Verrecchia, E., Manna, R. (2015). Epidemiology of FMF Worldwide. In: Gattorno, M. (eds) Familial Mediterranean Fever. Rare Diseases of the Immune System, vol 3. Springer, Cham. https://doi.org/10.1007/978-3-319-14615-7_5

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  • DOI: https://doi.org/10.1007/978-3-319-14615-7_5

  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-14614-0

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