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Common Adult Congenital Heart Disease Issues

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Cardiology Consult Manual

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Abstract

There are more adults than children living with congenital heart disease (CHD) in the United States. Most adults with congenital heart disease should be seen at least periodically by adult congenital heart disease (ACHD) specialists. The general cardiology consultant also has a unique opportunity to improve the care of patients with ACHD by improving access to care, while patients are interacting with the healthcare system for other reasons such as noncardiac surgery or pregnancy. This chapter describes the epidemiology of ACHD, issues with accessing healthcare, and transitioning patients from a pediatric to adult model of care. We will outline general approaches including society guidelines to common issues including hypertension, dyslipidemia, heart failure and transplantation, arrhythmias, liver disease, hyperviscosity, preoperative risk assessment, imaging, pregnancy, contraception, exercise, and infective endocarditis. Finally, we will briefly review some of the more commonly encountered forms of cyanotic and acyanotic ACHD and describe surgical treatments including shunts and the Fontan palliation procedure.

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Authors and Affiliations

  1. University of Rochester Medical Center/Cardiology, Rochester, NY, USA

    Erica O. Miller & James P. Eichelberger

Authors
  1. Erica O. Miller
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  2. James P. Eichelberger
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Correspondence to Erica O. Miller .

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Editors and Affiliations

  1. School of Medicine and Dentistry, University of Rochester Medical Center, Rochester, NY, USA

    Hanna Z. Mieszczanska

  2. Division of Cardiovascular Medicine-EP section, SUNY Downstate Medical Center, Brooklyn, NY, USA

    Adam S. Budzikowski

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Miller, E.O., Eichelberger, J.P. (2018). Common Adult Congenital Heart Disease Issues. In: Mieszczanska, H., Budzikowski, A. (eds) Cardiology Consult Manual. Springer, Cham. https://doi.org/10.1007/978-3-319-89725-7_11

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  • DOI: https://doi.org/10.1007/978-3-319-89725-7_11

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