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Cardiovascular Anesthesia for Adults with Congenital Heart Disease

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Intensive Care of the Adult with Congenital Heart Disease

Abstract

There are more adults living with congenital heart disease than children. Many of these adults with congenital heart disease (ACHD) will require a surgery or intervention, which may or not be related to their congenital heart disease (CHD). The successful anesthetic management of adults with CHD requires a stepwise approach to consider all the relevant factors. The perioperative management of ACHD patients requires a multidisciplinary team collaboration, and those with complex lesions should be cared for in centers with experience in CHD.

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References

  1. Egbe A, Uppu S, Lee S, Stroustrup A, Ho D, Srivastava S. Temporal variation of birth prevalence of congenital heart disease in the United States. Congenit Heart Dis. 2015;10(1):43–50.

    Article  PubMed  Google Scholar 

  2. Ntiloudi D, Giannakoulas G, Parcharidou D, Panagiotidis T, Gatzoulis MA, Karvounis H. Adult congenital heart disease: a paradigm of epidemiological change. Int J Cardiol. 2016;218:269–74.

    Article  PubMed  Google Scholar 

  3. Gilboa SM, Devine OJ, Kucik JE, Oster ME, Riehle-Colarusso T, Nembhard WN, et al. Congenital heart defects in the United States: estimating the magnitude of the affected population in 2010. Circulation. 2016;134(2):101–9.

    Article  PubMed  PubMed Central  Google Scholar 

  4. Marelli AJ, Ionescu-Ittu R, Mackie AS, Guo L, Dendukuri N, Kaouache M. Lifetime prevalence of congenital heart disease in the general population from 2000 to 2010. Circulation. 2014;130(9):749–56.

    Article  PubMed  Google Scholar 

  5. Apers S, Kovacs AH, Luyckx K, Thomet C, Budts W, Enomoto J, et al. Quality of life of adults with congenital heart disease in 15 countries: evaluating country-specific characteristics. J Am Coll Cardiol. 2016;67(19):2237–45.

    Article  PubMed  Google Scholar 

  6. Baehner T, Ellerkmann RK. Anesthesia in adults with congenital heart disease. Curr Opin Anaesthesiol. 2017;30(3):418–25.

    Article  PubMed  Google Scholar 

  7. Rouine-Rapp K, Russell IA, Foster E. Congenital heart disease in the adult. Int Anesthesiol Clin. 2012;50(2):16–39.

    Article  PubMed  Google Scholar 

  8. Nasr VG, Kussman BD. Advances in the care of adults with congenital heart disease. Semin Cardiothorac Vasc Anesth. 2015;19(3):175–86.

    Article  PubMed  Google Scholar 

  9. Cannesson M, Earing MG, Collange V, Kersten JR. Anesthesia for noncardiac surgery in adults with congenital heart disease. Anesthesiology. 2009;111(2):432–40.

    Article  PubMed  Google Scholar 

  10. Friesen RH. Anesthetic drugs in congenital heart disease. Semin Cardiothorac Vasc Anesth. 2014;18(4):363–70.

    Article  PubMed  Google Scholar 

  11. Maxwell BG, Wong JK, Kin C, Lobato RL. Perioperative outcomes of major noncardiac surgery in adults with congenital heart disease. Anesthesiology. 2013;119(4):762–9.

    Article  PubMed  Google Scholar 

  12. Maxwell BG, Posner KL, Wong JK, Oakes DA, Kelly NE, Domino KB, et al. Factors contributing to adverse perioperative events in adults with congenital heart disease: a structured analysis of cases from the closed claims project. Congenit Heart Dis. 2015;10(1):21–9.

    Article  PubMed  Google Scholar 

  13. Warnes CA, Williams RG, Bashore TM, Child JS, Connolly HM, Dearani JA, et al. ACC/AHA 2008 guidelines for the management of adults with congenital heart disease: executive summary: a report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (writing committee to develop guidelines for the management of adults with congenital heart disease). Circulation. 2008;118(23):2395–451.

    Article  PubMed  Google Scholar 

  14. Bhatt AB, Foster E, Kuehl K, Alpert J, Brabeck S, Crumb S, et al. Congenital heart disease in the older adult: a scientific statement from the American Heart Association. Circulation. 2015;131(21):1884–931.

    Article  PubMed  Google Scholar 

  15. Maxwell BG, Williams GD, Ramamoorthy C. Knowledge and attitudes of anesthesia providers about noncardiac surgery in adults with congenital heart disease. Congenit Heart Dis. 2014;9(1):45–53.

    Article  PubMed  Google Scholar 

  16. Greutmann M, Tobler D, Kovacs AH, Greutmann-Yantiri M, Haile SR, Held L, et al. Increasing mortality burden among adults with complex congenital heart disease. Congenit Heart Dis. 2015;10(2):117–27.

    Article  PubMed  Google Scholar 

  17. Escudero C, Khairy P, Sanatani S. Electrophysiologic considerations in congenital heart disease and their relationship to heart failure. + 2013;29(7):821–829.

    PubMed  Google Scholar 

  18. Bouchardy J, Therrien J, Pilote L, Ionescu-Ittu R, Martucci G, Bottega N, et al. Atrial arrhythmias in adults with congenital heart disease. Circulation. 2009;120(17):1679–86.

    Article  PubMed  Google Scholar 

  19. Loomba RS, Buelow MW, Aggarwal S, Arora RR, Kovach J, Ginde S. Arrhythmias in adults with congenital heart disease: what are risk factors for specific arrhythmias? Pacing Clin Electrophysiol. 2017;40(4):353–61.

    Article  PubMed  Google Scholar 

  20. Khairy P, Van Hare GF, Balaji S, Berul CI, Cecchin F, Cohen MI, et al. PACES/HRS expert consensus statement on the recognition and management of arrhythmias in adult congenital heart disease: developed in partnership between the Pediatric and Congenital Electrophysiology Society (PACES) and the Heart Rhythm Society (HRS). Endorsed by the governing bodies of PACES, HRS, the American College of Cardiology (ACC), the American Heart Association (AHA), the European Heart Rhythm Association (EHRA), the Canadian Heart Rhythm Society (CHRS), and the International Society for Adult Congenital Heart Disease (ISACHD). Heart Rhythm. 2014;11(10):e102–65.

    Article  PubMed  Google Scholar 

  21. Silka MJ, Hardy BG, Menashe VD, Morris CD. A population-based prospective evaluation of risk of sudden cardiac death after operation for common congenital heart defects. J Am Coll Cardiol. 1998;32(1):245–51.

    Article  CAS  PubMed  Google Scholar 

  22. Avila P, Chaix MA, Mondesert B, Khairy P. Sudden cardiac death in adult congenital heart disease. Card Electrophysiol Clin. 2017;9(2):225–34.

    Article  PubMed  Google Scholar 

  23. Koyak Z, de Groot JR, Bouma BJ, Zwinderman AH, Silversides CK, Oechslin EN, et al. Sudden cardiac death in adult congenital heart disease: can the unpredictable be foreseen? Europace. 2017;19(3):401–6.

    PubMed  Google Scholar 

  24. Navaratnam M, Dubin A. Pediatric pacemakers and ICDs: how to optimize perioperative care. Paediatr Anaesth. 2011;21(5):512–21.

    Article  PubMed  Google Scholar 

  25. Crossley GH, Poole JE, Rozner MA, Asirvatham SJ, Cheng A, Chung MK, et al. The Heart Rhythm Society (HRS)/American Society of Anesthesiologists (ASA) expert consensus statement on the perioperative management of patients with implantable defibrillators, pacemakers and arrhythmia monitors: facilities and patient management this document was developed as a joint project with the American Society of Anesthesiologists (ASA), and in collaboration with the American Heart Association (AHA), and the Society of Thoracic Surgeons (STS). Heart Rhythm. 2011;8(7):1114–54.

    Article  PubMed  Google Scholar 

  26. Stone ME, Salter B, Fischer A. Perioperative management of patients with cardiac implantable electronic devices. Br J Anaesth. 2011;107(Suppl 1):i16–26.

    Article  PubMed  Google Scholar 

  27. DeFilippis AP, Law K, Curtin S, Eckman JR. Blood is thicker than water: the management of hyperviscosity in adults with cyanotic heart disease. Cardiol Rev. 2007;15(1):31–4.

    Article  PubMed  Google Scholar 

  28. Jensen AS, Johansson PI, Idorn L, Sorensen KE, Thilen U, Nagy E, et al. The haematocrit—an important factor causing impaired haemostasis in patients with cyanotic congenital heart disease. Int J Cardiol. 2013;167(4):1317–21.

    Article  CAS  PubMed  Google Scholar 

  29. Tempe DK, Virmani S. Coagulation abnormalities in patients with cyanotic congenital heart disease. J Cardiothorac Vasc Anesth. 2002;16(6):752–65.

    Article  PubMed  Google Scholar 

  30. Horigome H, Hiramatsu Y, Shigeta O, Nagasawa T, Matsui A. Overproduction of platelet microparticles in cyanotic congenital heart disease with polycythemia. J Am Coll Cardiol. 2002;39(6):1072–7.

    Article  PubMed  Google Scholar 

  31. Cordina RL, Celermajer DS. Chronic cyanosis and vascular function: implications for patients with cyanotic congenital heart disease. Cardiol Young. 2010;20(3):242–53.

    Article  PubMed  Google Scholar 

  32. Oechslin E, Kiowski W, Schindler R, Bernheim A, Julius B, Brunner-La Rocca HP. Systemic endothelial dysfunction in adults with cyanotic congenital heart disease. Circulation. 2005;112(8):1106–12.

    Article  PubMed  Google Scholar 

  33. Khairy P, Aboulhosn J, Broberg CS, Cohen S, Cook S, Dore A, et al. Thromboprophylaxis for atrial arrhythmias in congenital heart disease: a multicenter study. Int J Cardiol. 2016;223:729–35.

    Article  PubMed  Google Scholar 

  34. Jensen AS, Idorn L, Norager B, Vejlstrup N, Sondergaard L. Anticoagulation in adults with congenital heart disease: the who, the when and the how? Heart. 2015;101(6):424–9.

    Article  CAS  PubMed  Google Scholar 

  35. Krieger EV, Leary PJ, Opotowsky AR. Pulmonary hypertension in congenital heart disease: beyond Eisenmenger syndrome. Cardiol Clin. 2015;33(4):599–609, ix.

    Article  PubMed  Google Scholar 

  36. Opotowsky AR. Clinical evaluation and management of pulmonary hypertension in the adult with congenital heart disease. Circulation. 2015;131(2):200–10.

    Article  PubMed  Google Scholar 

  37. Lowe BS, Therrien J, Ionescu-Ittu R, Pilote L, Martucci G, Marelli AJ. Diagnosis of pulmonary hypertension in the congenital heart disease adult population impact on outcomes. J Am Coll Cardiol. 2011;58(5):538–46.

    Article  PubMed  Google Scholar 

  38. Roth TS, Aboulhosn JA. Pulmonary hypertension and congenital heart disease. Cardiol Clin. 2016;34(3):391–400.

    Article  PubMed  Google Scholar 

  39. Bhamra-Ariza P, Keogh A, Muller D. Percutaneous interventional therapies for the treatment of patients with severe pulmonary hypertension. J Am Coll Cardiol. 2014;63(7):611–8.

    Article  PubMed  Google Scholar 

  40. Baruteau AE, Serraf A, Levy M, Petit J, Bonnet D, Jais X, et al. Potts shunt in children with idiopathic pulmonary arterial hypertension: long-term results. Ann Thorac Surg. 2012;94(3):817–24.

    Article  PubMed  Google Scholar 

  41. Hickey PR, Hansen DD, Wessel DL, Lang P, Jonas RA. Pulmonary and systemic hemodynamic responses to fentanyl in infants. Anesth Analg. 1985;64(5):483–6.

    Article  CAS  PubMed  Google Scholar 

  42. Williams GD, Philip BM, Chu LF, Boltz MG, Kamra K, Terwey H, et al. Ketamine does not increase pulmonary vascular resistance in children with pulmonary hypertension undergoing sevoflurane anesthesia and spontaneous ventilation. Anesth Analg. 2007;105(6):1578–84, table of contents.

    Article  CAS  PubMed  Google Scholar 

  43. Berman W Jr, Fripp RR, Rubler M, Alderete L. Hemodynamic effects of ketamine in children undergoing cardiac catheterization. Pediatr Cardiol. 1990;11(2):72–6.

    Article  PubMed  Google Scholar 

  44. Friesen RH, Nichols CS, Twite MD, Cardwell KA, Pan Z, Pietra B, et al. The hemodynamic response to dexmedetomidine loading dose in children with and without pulmonary hypertension. Anesth Analg. 2013;117(4):953–9.

    Article  CAS  PubMed  Google Scholar 

  45. Chang AC, Zucker HA, Hickey PR, Wessel DL. Pulmonary vascular resistance in infants after cardiac surgery: role of carbon dioxide and hydrogen ion. Crit Care Med. 1995;23(3):568–74.

    Article  CAS  PubMed  Google Scholar 

  46. Morray JP, Lynn AM, Mansfield PB. Effect of pH and PCO2 on pulmonary and systemic hemodynamics after surgery in children with congenital heart disease and pulmonary hypertension. J Pediatr. 1988;113(3):474–9.

    Article  CAS  PubMed  Google Scholar 

  47. Rudolph AM, Yuan S. Response of the pulmonary vasculature to hypoxia and H+ ion concentration changes. J Clin Invest. 1966;45(3):399–411.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  48. Hickey PR, Hansen DD, Wessel DL, Lang P, Jonas RA, Elixson EM. Blunting of stress responses in the pulmonary circulation of infants by fentanyl. Anesth Analg. 1985;64(12):1137–42.

    Article  CAS  PubMed  Google Scholar 

  49. Ivy DD. Prostacyclin in the intensive care setting. Pediatr Crit Care Med. 2010;11(2 Suppl):S41–5.

    Article  PubMed  PubMed Central  Google Scholar 

  50. Barrington KJ, Finer NN, Chan WK. A blind, randomized comparison of the circulatory effects of dopamine and epinephrine infusions in the newborn piglet during normoxia and hypoxia. Crit Care Med. 1995;23(4):740–8.

    Article  CAS  PubMed  Google Scholar 

  51. McGovern JJ, Cheifetz IM, Craig DM, Bengur AR, Quick G, Ungerleider RM, et al. Right ventricular injury in young swine: effects of catecholamines on right ventricular function and pulmonary vascular mechanics. Pediatr Res. 2000;48(6):763–9.

    Article  CAS  PubMed  Google Scholar 

  52. Jaillard S, Elbaz F, Bresson-Just S, Riou Y, Houfflin-Debarge V, Rakza T, et al. Pulmonary vasodilator effects of norepinephrine during the development of chronic pulmonary hypertension in neonatal lambs. Br J Anaesth. 2004;93(6):818–24.

    Article  CAS  PubMed  Google Scholar 

  53. Koizumi T, Hermo CI, Bjertnaes LJ, Banerjee M, Newman JH, Kubo K. Nitric oxide and nitroglycerin reversal of pulmonary vasoconstriction induced by alpha-activation during exercise. Am J Phys. 1996;270(3 Pt 2):H875–80.

    CAS  Google Scholar 

  54. Kondo U, Kim SO, Nakayama M, Murray PA. Pulmonary vascular effects of propofol at baseline, during elevated vasomotor tone, and in response to sympathetic alpha- and beta-adrenoreceptor activation. Anesthesiology. 2001;94(5):815–23.

    Article  CAS  PubMed  Google Scholar 

  55. Mastropietro CW, Clark JA, Delius RE, Walters HL 3rd, Sarnaik AP. Arginine vasopressin to manage hypoxemic infants after stage I palliation of single ventricle lesions. Pediatr Crit Care Med. 2008;9(5):506–10.

    Article  PubMed  Google Scholar 

  56. Kalambokis GN, Pappas K, Tsianos EV. Terlipressin improves pulmonary pressures in cirrhotic patients with pulmonary hypertension and variceal bleeding or hepatorenal syndrome. Hepatobiliary Pancreat Dis Int. 2012;11(4):434–7.

    Article  CAS  PubMed  Google Scholar 

  57. Alshawabkeh LI, Opotowsky AR. Burden of heart failure in adults with congenital heart disease. Curr Heart Fail Rep. 2016;13(5):247–54.

    Article  PubMed  Google Scholar 

  58. Engelings CC, Helm PC, Abdul-Khaliq H, Asfour B, Bauer UM, Baumgartner H, et al. Cause of death in adults with congenital heart disease—an analysis of the German National Register for Congenital Heart Defects. Int J Cardiol. 2016;211:31–6.

    Article  PubMed  Google Scholar 

  59. Tutarel O. Acquired heart conditions in adults with congenital heart disease: a growing problem. Heart. 2014;100(17):1317–21.

    Article  PubMed  Google Scholar 

  60. O'Leary JM, Siddiqi OK, de Ferranti S, Landzberg MJ, Opotowsky AR. The changing demographics of congenital heart disease hospitalizations in the United States, 1998 through 2010. JAMA. 2013;309(10):984–6.

    Article  CAS  PubMed  Google Scholar 

  61. Opotowsky AR, Siddiqi OK, Webb GD. Trends in hospitalizations for adults with congenital heart disease in the U.S. J Am Coll Cardiol. 2009;54(5):460–7.

    Article  PubMed  Google Scholar 

  62. Stout KK, Broberg CS, Book WM, Cecchin F, Chen JM, Dimopoulos K, et al. Chronic heart failure in congenital heart disease: a scientific statement from the American Heart Association. Circulation. 2016;133(8):770–801.

    Article  PubMed  Google Scholar 

  63. Norozi K, Wessel A, Alpers V, Arnhold JO, Geyer S, Zoege M, et al. Incidence and risk distribution of heart failure in adolescents and adults with congenital heart disease after cardiac surgery. Am J Cardiol. 2006;97(8):1238–43.

    Article  PubMed  Google Scholar 

  64. Rosenthal DN, Hammer GB. Cardiomyopathy and heart failure in children: anesthetic implications. Paediatr Anaesth. 2011;21(5):577–84.

    Article  PubMed  Google Scholar 

  65. Bouma BJ, Mulder BJ. Changing landscape of congenital heart disease. Circ Res. 2017;120(6):908–22.

    Article  CAS  PubMed  Google Scholar 

  66. Afilalo J, Therrien J, Pilote L, Ionescu-Ittu R, Martucci G, Marelli AJ. Geriatric congenital heart disease: burden of disease and predictors of mortality. J Am Coll Cardiol. 2011;58(14):1509–15.

    Article  PubMed  Google Scholar 

  67. Rajpal S, Alshawabkeh L, Opotowsky AR. Current role of blood and urine biomarkers in the clinical care of adults with congenital heart disease. Curr Cardiol Rep. 2017;19(6):50.

    Article  PubMed  Google Scholar 

  68. Eindhoven JA, van den Bosch AE, Jansen PR, Boersma E, Roos-Hesselink JW. The usefulness of brain natriuretic peptide in complex congenital heart disease: a systematic review. J Am Coll Cardiol. 2012;60(21):2140–9.

    Article  CAS  PubMed  Google Scholar 

  69. Eindhoven JA, van den Bosch AE, Boersma E, Roos-Hesselink JW. The usefulness of brain natriuretic peptide in simple congenital heart disease—a systematic review. Cardiol Young. 2013;23(3):315–24.

    Article  PubMed  Google Scholar 

  70. Popelova J, Kotaska K, Cerny S, Prokopova M, Rubacek M. Range and distribution of NT-proBNP values in stable corrected congenital heart disease of various types. Can J Cardiol. 2012;28(4):471–6.

    Article  CAS  PubMed  Google Scholar 

  71. Davies RR, Russo MJ, Yang J, Quaegebeur JM, Mosca RS, Chen JM. Listing and transplanting adults with congenital heart disease. Circulation. 2011;123(7):759–67.

    Article  PubMed  Google Scholar 

  72. Alshawabkeh LI, Hu N, Carter KD, Opotowsky AR, Light-McGroary K, Cavanaugh JE, et al. Wait-list outcomes for adults with congenital heart disease listed for heart transplantation in the U.S. J Am Coll Cardiol. 2016;68(9):908–17.

    Article  PubMed  Google Scholar 

  73. Dinardo JA. Heart failure associated with adult congenital heart disease. Semin Cardiothorac Vasc Anesth. 2013;17(1):44–54.

    Article  PubMed  Google Scholar 

  74. Harper AR, Crossland DS, Perri G, O'Sullivan JJ, Chaudhari MP, Schueler S, et al. Is alternative cardiac surgery an option in adults with congenital heart disease referred for thoracic organ transplantation? Eur J Cardiothorac Surg. 2013;43(2):344–51.

    Article  PubMed  Google Scholar 

  75. Joyce DL, Crow SS, John R, St Louis JD, Braunlin EA, Pyles LA, et al. Mechanical circulatory support in patients with heart failure secondary to transposition of the great arteries. J Heart Lung Transplant. 2010;29(11):1302–5.

    Article  PubMed  Google Scholar 

  76. Baumgartner H, Bonhoeffer P, De Groot NM, de Haan F, Deanfield JE, Galie N, et al. ESC guidelines for the management of grown-up congenital heart disease (new version 2010). Eur Heart J. 2010;31(23):2915–57.

    Article  PubMed  Google Scholar 

  77. Knirsch W, Nadal D. Infective endocarditis in congenital heart disease. Eur J Pediatr. 2011;170(9):1111–27.

    Article  PubMed  Google Scholar 

  78. Wilson W, Taubert KA, Gewitz M, Lockhart PB, Baddour LM, Levison M, et al. Prevention of infective endocarditis: guidelines from the American Heart Association: a guideline from the American Heart Association Rheumatic Fever, Endocarditis, and Kawasaki Disease Committee, Council on Cardiovascular Disease in the Young, and the Council on Clinical Cardiology, Council on Cardiovascular Surgery and Anesthesia, and the Quality of Care and Outcomes Research Interdisciplinary Working Group. Circulation. 2007;116(15):1736–54.

    Article  PubMed  Google Scholar 

  79. Habib G, Hoen B, Tornos P, Thuny F, Prendergast B, Vilacosta I, et al. Guidelines on the prevention, diagnosis, and treatment of infective endocarditis (new version 2009): the Task Force on the Prevention, Diagnosis, and Treatment of Infective Endocarditis of the European Society of Cardiology (ESC). Endorsed by the European Society of Clinical Microbiology and Infectious Diseases (ESCMID) and the International Society of Chemotherapy (ISC) for Infection and Cancer. Eur Heart J. 2009;30(19):2369–413.

    Article  PubMed  Google Scholar 

  80. Richey R, Wray D, Stokes T, Guideline Development G. Prophylaxis against infective endocarditis: summary of NICE guidance. BMJ. 2008;336(7647):770–1.

    Article  PubMed  PubMed Central  Google Scholar 

  81. Thornhill MH, Dayer M, Lockhart PB, Prendergast B. Antibiotic prophylaxis of infective endocarditis. Curr Infect Dis Rep. 2017;19(2):9.

    Article  PubMed  PubMed Central  Google Scholar 

  82. Duval X, Delahaye F, Alla F, Tattevin P, Obadia JF, Le Moing V, et al. Temporal trends in infective endocarditis in the context of prophylaxis guideline modifications: three successive population-based surveys. J Am Coll Cardiol. 2012;59(22):1968–76.

    Article  PubMed  Google Scholar 

  83. Pasquali SK, He X, Mohamad Z, McCrindle BW, Newburger JW, Li JS, et al. Trends in endocarditis hospitalizations at US children's hospitals: impact of the 2007 American Heart Association Antibiotic Prophylaxis Guidelines. Am Heart J. 2012;163(5):894–9.

    Article  PubMed  PubMed Central  Google Scholar 

  84. Dayer M, Thornhill M. Antibiotic prophylaxis guidelines and infective endocarditis: cause for concern? J Am Coll Cardiol. 2015;65(19):2077–8.

    Article  PubMed  Google Scholar 

  85. Dayer MJ, Jones S, Prendergast B, Baddour LM, Lockhart PB, Thornhill MH. Incidence of infective endocarditis in England, 2000–13: a secular trend, interrupted time-series analysis. Lancet. 2015;385(9974):1219–28.

    Article  PubMed  Google Scholar 

  86. Mackie AS, Liu W, Savu A, Marelli AJ, Kaul P. Infective endocarditis hospitalizations before and after the 2007 American Heart Association Prophylaxis Guidelines. + 2016;32(8):942–948.

    Google Scholar 

  87. Habib G, Lancellotti P, Antunes MJ, Bongiorni MG, Casalta JP, Del Zotti F, et al. 2015 ESC guidelines for the management of infective endocarditis: the Task Force for the Management of Infective Endocarditis of the European Society of Cardiology (ESC). Endorsed by: European Association for Cardio-Thoracic Surgery (EACTS), the European Association of Nuclear Medicine (EANM). Eur Heart J. 2015;36(44):3075–128.

    Article  PubMed  Google Scholar 

  88. Fontan F, Baudet E. Surgical repair of tricuspid atresia. Thorax. 1971;26(3):240–8.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  89. Fontan F, Kirklin JW, Fernandez G, Costa F, Naftel DC, Tritto F, et al. Outcome after a “perfect” Fontan operation. Circulation. 1990;81(5):1520–36.

    Article  CAS  PubMed  Google Scholar 

  90. Walker F. Pregnancy and the various forms of the Fontan circulation. Heart. 2007;93(2):152–4.

    Article  PubMed  Google Scholar 

  91. d'Udekem Y, Iyengar AJ, Galati JC, Forsdick V, Weintraub RG, Wheaton GR, et al. Redefining expectations of long-term survival after the Fontan procedure: twenty-five years of follow-up from the entire population of Australia and New Zealand. Circulation. 2014;130(11 Suppl 1):S32–8.

    Article  PubMed  Google Scholar 

  92. Alsaied T, Alsidawi S, Allen CC, Faircloth J, Palumbo JS, Veldtman GR. Strategies for thromboprophylaxis in Fontan circulation: a meta-analysis. Heart. 2015;101(21):1731–7.

    Article  CAS  PubMed  Google Scholar 

  93. Gnanappa GK, Celermajer DS, Sholler GF, Gentles T, Winlaw D, d'Udekem Y, et al. The long-term management of children and adults with a Fontan circulation: a systematic review and survey of current practice in Australia and New Zealand. Pediatr Cardiol. 2017;38(1):56–69.

    Article  PubMed  Google Scholar 

  94. Sridhar A, Giamberti A, Foresti S, Cappato R, Garcia CR, Cabrera ND, et al. Fontan conversion with concomitant arrhythmia surgery for the failing atriopulmonary connections: mid-term results from a single centre. Cardiol Young. 2011;21(6):665–9.

    Article  PubMed  Google Scholar 

  95. Mossad EB, Motta P, Vener DF. Anesthetic considerations for adults undergoing Fontan conversion surgery. Anesthesiol Clin. 2013;31(2):405–19.

    Article  PubMed  Google Scholar 

  96. Opotowsky AR, Siddiqi OK, D'Souza B, Webb GD, Fernandes SM, Landzberg MJ. Maternal cardiovascular events during childbirth among women with congenital heart disease. Heart. 2012;98(2):145–51.

    Article  PubMed  Google Scholar 

  97. Roos-Hesselink JW, Ruys TP, Stein JI, Thilen U, Webb GD, Niwa K, et al. Outcome of pregnancy in patients with structural or ischaemic heart disease: results of a registry of the European Society of Cardiology. Eur Heart J. 2013;34(9):657–65.

    Article  PubMed  Google Scholar 

  98. Siu SC, Sermer M, Colman JM, Alvarez AN, Mercier LA, Morton BC, et al. Prospective multicenter study of pregnancy outcomes in women with heart disease. Circulation. 2001;104(5):515–21.

    Article  CAS  PubMed  Google Scholar 

  99. Canobbio MM, Warnes CA, Aboulhosn J, Connolly HM, Khanna A, Koos BJ, et al. Management of pregnancy in patients with complex congenital heart disease: a scientific statement for healthcare professionals from the American Heart Association. Circulation. 2017;135(8):e50–87.

    Article  PubMed  Google Scholar 

  100. Greutmann M, Pieper PG. Pregnancy in women with congenital heart disease. Eur Heart J. 2015;36(37):2491–9.

    Article  PubMed  Google Scholar 

  101. Fernandes SM, Arendt KW, Landzberg MJ, Economy KE, Khairy P. Pregnant women with congenital heart disease: cardiac, anesthetic and obstetrical implications. Expert Rev Cardiovasc Ther. 2010;8(3):439–48.

    Article  PubMed  Google Scholar 

  102. Ortman AJ. The pregnant patient with congenital heart disease. Semin Cardiothorac Vasc Anesth. 2012;16(4):220–34.

    Article  PubMed  Google Scholar 

  103. Cecchin F, Halpern DG. Cardiac arrhythmias in adults with congenital heart disease: pacemakers, implantable cardiac defibrillators, and cardiac resynchronization therapy devices. Card Electrophysiol Clin. 2017;9(2):319–28.

    Article  PubMed  Google Scholar 

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Twite, M., Ing, R., Schwartz, L. (2019). Cardiovascular Anesthesia for Adults with Congenital Heart Disease. In: da Cruz, E., Macrae, D., Webb, G. (eds) Intensive Care of the Adult with Congenital Heart Disease. Congenital Heart Disease in Adolescents and Adults. Springer, Cham. https://doi.org/10.1007/978-3-319-94171-4_7

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  • DOI: https://doi.org/10.1007/978-3-319-94171-4_7

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-94170-7

  • Online ISBN: 978-3-319-94171-4

  • eBook Packages: MedicineMedicine (R0)

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