The initial cases of DM in German literature were fatal [1–3], but recoveries were soon observed [4, 5]. In the precorticosteroid era, the largest review, of 153 cases with adequate follow-up, determined a mortality rate of 61% [6]. Most surviving patients had permanent sequelae (e.g., muscle atrophy, joint contractures, and calcinosis). Later, in more studies of noncorticosteroid-treated patients, the mortality rate improved to 37%, and 33% of patients had good recoveries [7–9]. However, the prognosis of DM was significantly worse in older patients.
In contrast, case reports of “spontaneous” recoveries are documented in classic DM [4–6] and amyopathic DM [10].
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(2009). Evolution and prognosis of Dermatomyositis. In: Dermatomyositis. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-540-79313-7_42
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