Abstract
Otosclerosis is a disorder of the bony labyrinth and exclusively affects human beings. In otosclerosis the ivory-like enchondral bone of the otic capsule is replaced by immature and spongy new bone, and this process of remodeling occurs continuously. The process can become quiescent at anytime or may become reactivated, in a way that oto sclerotic foci commonly contain both active and inactive regions (SCHUKNECHT 1993a). Unilateral involvement is seen in only approximately 10-15% of the cases and there is a 2:1 female preponderance. The risk to an affected person of having a child who will eventually develop otosclerosis is 1 in 4 (DONNELL and ALFI 1980; SHIN et al. 2001). In comparison with patients with a sporadic form of otosclerosis, the radiologic lesions are more often detectable, bilateral, and severe in the familial forms (SHIN et al. 2001).
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Lemmerling, M. (2004). Otosclerosis. In: Lemmerling, M., Kollias, S.S. (eds) Radiology of the Petrous Bone. Medical Radiology. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-18836-7_7
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DOI: https://doi.org/10.1007/978-3-642-18836-7_7
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