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Prionkrankheiten (transmissible spongiforme Enzephalopathien)

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Neuropathologie

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Zusammenfassung

Prionkrankheiten sind übertragbare neurodegenerative Krankheiten, die bei Mensch und Tier auftreten (Prusiner 1998) (Tabellen 11.1–11.3). Klinisch gehen sie mit einer meist stark ausgeprägten Demenz und verschiedenen neurologischen Veränderungen wie Ataxie, Myoklonien oder Erblindung einher; sie nehmen immer einen tödlichen Verlauf.

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Authors
  1. H. A. Kretzschmar
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Editors and Affiliations

  1. Haldenbachstr. 17, 72074, Tübingen, Germany

    Jürgen Peiffer (Nervenarzt und Neuropathologe ehem. Direktor des Institutes für Hirnforschung der Universität) (Nervenarzt und Neuropathologe ehem. Direktor des Institutes für Hirnforschung der Universität)

  2. Institut für Neuropathologie, Universitätsklinikum der Rheinisch-Westfälischen Technischen Hochschule Aachen, Pauwelsstraße 30, 52074, Aachen, Germany

    J. Michael Schröder

  3. Institut für Neuropathologie, Universitätsklinikum Münster, Domagkstr. 19, 48149, Münster, Germany

    Werner Paulus

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© 2002 Springer-Verlag Berlin Heidelberg

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Kretzschmar, H.A. (2002). Prionkrankheiten (transmissible spongiforme Enzephalopathien). In: Peiffer, J., Schröder, J.M., Paulus, W. (eds) Neuropathologie. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-59371-0_11

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  • DOI: https://doi.org/10.1007/978-3-642-59371-0_11

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-63951-7

  • Online ISBN: 978-3-642-59371-0

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