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Xeroderma Pigmentosum Patients from Germany (the Mannheim XP Collection): Clinical and Biochemical Characteristics

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Skin Carcinogenesis in Man and in Experimental Models

Part of the book series: Recent Results in Cancer Research ((RECENTCANCER,volume 128))

Abstract

I am assuming that most readers are familiar with the human genodermatosis xeroderma pigmentosum (XP). It is a rare genetic disease with hypersensitivity to ultraviolet (UV) radiation and numerous malignancies on sun-exposed areas of the skin and the eye because of an inability to repair DNA damage inflicted by harmful UV radiation.

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Authors and Affiliations

  1. German Cancer Research Center, W-6900, Heidelberg, Fed. Rep. of Germany

    H. W. Thielmann

Authors
  1. H. W. Thielmann
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Editor information

Editors and Affiliations

  1. Division: Mechanisms of Tumorigenesis, Research Program 3: Risk Factors of Cancer and Cancer Prevention, Deutsches Krebsforschungszentrum, Im Neuenheimer Feld 280, W-6900, Heidelberg, Germany

    Erich Hecker

  2. Department of Dermatology, Mannheim Medical School, University of Heidelberg, Postfach 10 80 23, Theodor-Kutzer-Ufer, W-6800, Mannheim, Germany

    E. G. Jung (Director) (Director)

  3. Division: Biochemistry of Tissue Specific Regulation, Research Program 2: Tumor Cell Regulation, Deutsches Krebsforschungszentrum, Im Neuenheimer Feld 280, W-6900, Heidelberg, Germany

    F. Marks

  4. Department of Dermatology, University of Heidelberg, Voss-Str. 2, W-6900, Heidelberg, Germany

    W. Tilgen

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© 1993 Springer-Verlag Berlin · Heidelberg

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Thielmann, H.W. (1993). Xeroderma Pigmentosum Patients from Germany (the Mannheim XP Collection): Clinical and Biochemical Characteristics. In: Hecker, E., Jung, E.G., Marks, F., Tilgen, W. (eds) Skin Carcinogenesis in Man and in Experimental Models. Recent Results in Cancer Research, vol 128. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-84881-0_21

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  • DOI: https://doi.org/10.1007/978-3-642-84881-0_21

  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-642-84883-4

  • Online ISBN: 978-3-642-84881-0

  • eBook Packages: Springer Book Archive

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