Abstract
The primary immunodeficiency diseases (PIDs) are a heterogeneous group of inherited disorders with defects in one or more components of the immune system. PIDs are classified into T lymphocyte, B lymphocyte, phagocytic cell, and complement deficiencies. This classification is simple and practical because clinical symptoms, mainly susceptibility to infections, vary according to the affected arm of the immune system. The prognosis of these disorders and their treatment depends on their early recognition and initiation of appropriate management.
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Plebani, A., Chirico, G. (2012). Congenital Immunodeficiencies. In: Buonocore, G., Bracci, R., Weindling, M. (eds) Neonatology. Springer, Milano. https://doi.org/10.1007/978-88-470-1405-3_109
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DOI: https://doi.org/10.1007/978-88-470-1405-3_109
Publisher Name: Springer, Milano
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