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Diagnosis and Treatment of the Congenital Long Qt Syndrome

  • Chapter
Cardiovascular Genetics for Clinicians

Part of the book series: Developments in Cardiovascular Medicine ((DICM,volume 239))

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Abstract

Over the past decade, the congenital long QT syndrome (LQTS) has contributed significantly to our understanding of ventricular arrhythmias. Congenital LQTS is an inherited disease characterized by prolonged ventricular repolarization and a propensity for life-threatening ventricular tachyarrhythmias resulting in syncope and sudden death [1]. Two forms of inherited long QT syndrome are known: (1) the more common Romano-Ward syndrome (RWS), with an autosomal dominant inheritance, and (2) the Jervell and Lange-Nielssen syndrome (JLN), which is usually autosomal recessive long QT syndrome associated with inherited sensorineuronal deafness. Long QT syndrome, occurring secondary to heart failure, hypertrophy or drug-therapy, is called acquired LQTS [2].

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Authors
  1. X. H. T. Wehrens
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  2. M. A. Vos
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  3. A. A. Wilde
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Editor information

Editors and Affiliations

  1. Academic Hospital Maastricht, Maastricht, The Netherlands

    P. A. Doevendans

  2. Academic Medical Center, Amsterdam, The Netherlands

    A. A. M. Wilde

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© 2001 Springer Science+Business Media Dordrecht

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Wehrens, X.H.T., Vos, M.A., Wilde, A.A. (2001). Diagnosis and Treatment of the Congenital Long Qt Syndrome. In: Doevendans, P.A., Wilde, A.A.M. (eds) Cardiovascular Genetics for Clinicians. Developments in Cardiovascular Medicine, vol 239. Springer, Dordrecht. https://doi.org/10.1007/978-94-010-1019-1_15

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  • DOI: https://doi.org/10.1007/978-94-010-1019-1_15

  • Publisher Name: Springer, Dordrecht

  • Print ISBN: 978-94-010-3888-1

  • Online ISBN: 978-94-010-1019-1

  • eBook Packages: Springer Book Archive

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